Malformasi Anorektal. ANGKA KEBERHASILAN POSTEROSAGITTAL ANORECTOPLASTY (PSARP) YANG DINILAI DARI SKOR KLOTZ PADA PASIEN MALFORMASI ANOREKTAL. Faktor Risiko yang Memengaruhi Luaran Klinis Malformasi Anorektal pada Neonatus di RSUD Dr. Zainoel Abidin, Banda Aceh. Article. Full-text available.

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Performance of a new pull-through operation should be avoided so that the patient’s rectal malformssi is preserved. Etiology Anorectal malformations ARM represent a spectrum of abnormalities ranging from mild anal anomalies to complex cloacal malformations.

Anorectal malformations

This prevents formation of a megasigmoid, which may be responsible for the future development of constipation. Depending on the amount of colon resected, the patient may have loose stools.

A contrast enema is helpful in differentiating these two groups of patients. Urinary continence Urinary incontinence occurs in male patients with anorectal malformations only when they have an extremely defective or absent sacrum, or when the basic principles of surgical repair are not followed and important nerves are damaged during the operation. Laparoscopically-assisted anorectal repair avalah either be performed in anoreital newborn period without a colostomy or in a stage-approach.

The hydrostatic pressure must be high enough manual syringe injection to overcome the muscle tone of the striated muscle mechanism that surrounds the rectum and keeps it collapsed.

The rectum and vagina share a common wall and the vagina and urinary tract likewise have a common wall. When performing the colostomy in the newborn, the distal amorektal should be irrigated to remove all of the meconium.

Malformasi Anorektal | Lokananta | Jurnal Kedokteran Meditek

First; are there associated anomalies that threaten the baby’s life and should be dealt with right away?

After colostomy closure, severe diaper rash is common because the perineal skin has never before been exposed to stool. The early management of a newborn infant born with an anorectal anomaly is crucial and two important questions must be answered during the first 24 to 48 hours of life. The descending colon with normal caliber and normal motility is anastomosed to the rectum at the peritoneal reflection.


If catherization anorrktal not performed, overflow incontinence occurs.

Fecal continence Fecal continence depends on three main factors: Long-term outcomes of anorectal malformations. The repair of persistent cloacas represents a serious technical challenge that should be performed in specialized centers by pediatric surgeons anorekgal to the care of these complicated patients [ 22 ]. Both the urinary tract and the distended vagina may need to be dealt with in the newborn period to avoid serious complications. Spinal ultrasound in the first 3 months of life and magnetic resonance imaging thereafter are useful radiologic modalities to establish the diagnosis.

Anorectal malformations

This article has been corrected. Complex vaginal mobilizations are often required and frequenly a vaginal replacement with small intestine or colon is necessary. As early as the s, it was recognized that there was an increased risk for a sibling of a patient with ARM to be born with a malformation, as much as 1 incompared with the incidence of about 1 in in the general population. Those that survived most likely suffered from a type of defect that would now be recognized as “low”.

Early decision-making The early management of a newborn infant born with an anorectal anomaly is crucial and two important questions must be answered during the first 24 to 48 hours of life. During the first 60 years of the 20th century, surgeons performed a perineal operation without a colostomy for the so-called low malformations.

The patients must be followed regularly, and laxatives and dietary manipulations are begun at the first sign of constipation.

Clinical presentation Classification Comparing the results of reported series has always been a problem with anorectal malformations because different surgeons use different terminology when referring to malfornasi of imperforate anus. Better imaging techniques, and a better knowledge of the anatomy and physiology of the pelvic structures at birth have refined diagnosis and initial management, and the analysis of large series of patients allows better prediction of associated anomalies and functional prognosis.

Table 2 Detailed classification of anorectal malformations ARM.

Except for patients with rectal atresia, most patients with anorectal malformations are born without an anal canal; therefore, sensation does not exist or is rudimentary. The laparoscopically-assisted anorectal approach consists in mobilizing and bringing the rectum through the pelvic floor sphincter muscles through a minimal posterior incision.


This new technique, described by KE Georgeson et al. So, the actual impact of tethered cord itself on their functional prognosis is unclear. At two weeks postoperatively, anal calibration is performed, followed by a program of anal dilitations.

These babies should undergo colostomy at birth, and then their definitive repair involves a posterior sagittal approach and an end-to-end anastomosis between the upper rectal pouch and the anal canal. The goals of surgical treatment are to achieve bowel control, urinary control, and normal sexual function. Such children need supervision to avoid fecal impaction, constipation, and soiling.

To avoid this, the distal stoma must be made intentionally small, as it will be used only for irrigations and radiologic studies.

It seems that patients can perceive distention of the rectum but this requires a rectum that has been properly located within the muscle structures. Hydrosoluble contrast material is injected into the distal stoma to demonstrate the precise location of the distal rectum and its likely urinary communication.

Several pitfalls exist with regard to the creation of the colostomy. Decision-making for male newborns Male newborns with recto-perineal fistula do not need a colostomy.

Episodes of soiling are usually related to constipation, and when constipation is treated properly, the soiling frequently disappears. Operative Management of Anomalies in Male. The program, although simplistic, is implemented by trial and error over a period of one week. The fistula and lower part of the rectum are carefully dissected to permit mobilization of maoformasi rectum for backward placement within the limits of the sphincter complex.

Gynecologic concerns anorektla the treatment of teenagers with cloaca. When these girls were examined, the little pouch of what used to be the rectum was found opening into the vestibule, indicating that these patients were been born with a rectovestibular fistula.